Saves the questions and what to expect into your notes, next to the visit they belong to.
Keep this study
Lead
Association for Pediatric Pulmonary Hypertension
Age
0–18
Sex
ALL
Healthy volunteers
Not accepted
You may be eligible if
Patient must be an incident patient, i.e.newly diagnosed with PH
Age at time of diagnosis is at least 3 months and less than 18 years
Patients must present with PH belonging to one of the following categories
* Group 1 according to updated Nice clinical classification
* Group 3 according to updated Nice clinical classification
* Group 4 according to updated Nice clinical classification
* Group 5 according to updated Nice clinical classification
PH confirmed by heart catheterisation (HC)
At HC, the patient must present with mean pulmonary arterial pressure (PAP) of at least 25 mmHg at rest, a pulmonary vascular resistance index (PVRi) equal to or below 3 Wood units\*m\^2 and mean pulmonary arterial wedge pressure (PAWP) below or equal to 15 mmHg
In case of congenital heart disease (CHD) patients who had undergone palliative procedure or repair to close systemic to pulmonary shunt, the diagnosis of PH must have been confirmed by HC at least 6 months after surgery/palliative procedure took place
For patients with PAH-CHD open shunt, only those considered not operable due to advanced pulmonary vascular disease are eligible
Patients to be included into the registry, and/or their legal guardians, must give informed consent. Where applicable patients will be asked for their written assent
Participating sites must agree to adhere to the recommendations of the WSPH 2015 Nice, Pediatric Taskforce.
You may not be if
Patients belonging to Group 2 according to updated Nice clinical classification
