APAH with congenital heart defects with / without Eisenmenger syndrome (WHO functional class II-IV), invasively diagnosed by right heart and left heart catheterization: mean pulmonary arterial pressure (mPAP) ≥ 25 mmHg, with targeted PAH medication for at least two months stable before study inclusion (exception: compensated WHO class II without vasodilating drug therapy)
You may not be if
Pregnancy or lactation
Change in medication during the last 2 months
severe walking disturbance
uncertain diagnoses
No previous invasively confirmation of PH
acute diseases, infections, fever
Serious lung disease with FEV1 \<50% or TLC \<70% of target
